114年:醫學四(2)

下列何者不是視神經脊髓炎( neuromyelitis optica spectrum disorder )的核心臨床病症( core clinical characteristics )?

A最後區症候群( area postrema syndrome )
B失語症( aphasia)
C視神經炎( optic neuritis )
D急性脊髓炎( acute myelitis )

詳細解析

本題觀念:

2015 年 International Panel for NMO Diagnosis (IPND) 訂定之 neuromyelitis optica spectrum disorder (NMOSD) 國際共識診斷準則將「核心臨床病症」(core clinical characteristics)列為 6 大類:

  1. optic neuritis
  2. acute myelitis
  3. area postrema syndrome(無明顯原因的頑固性打嗝、噁心或嘔吐)
  4. acute brainstem syndrome
  5. symptomatic narcolepsy 或其他具典型影像的 diencephalic syndrome
  6. symptomatic cerebral syndrome 伴有 NMOSD 典型腦部病灶 (neurology.org, [wearesrna.org](https://wearesrna.org/living-with-myelitis/disease-information/neuromyelitis-optica-spectr

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