106年:內專
下列有關血管炎症候群(vasculitis syndrome)與臨床相關的配對中,何者最正確?(1)Granulomatosis with polyangiitis-usually cANCA (+);(2)Takayasu arteritis-difference in bilateral. brachial blood pressure;(3)Giant cell arteritis-high incidence in young age group;(4)Eosinophilic granulomatosis with polyangiitis-high incidence in old age group;(5)Henoch-Schonlein purpura-increase in serum IgA;(6)Polyarteritis nodosa-chronic pancreatitis;(7)Cryoglobulinemic vasculitis-associated with hepatitis C;(8)Behcet's disease-usually pANCA (+);(9)Microscopic polyangiitis-usually associated with sinusitis
A(1)+(2)+(3)
B(3)+(4)+(6)
C(1)+(5)+(7)
D(2)+(7)+(8)
E(1)+(3)+(9)
詳細解析
本題觀念:
血管炎症候群分類與其典型臨床、實驗室檢查(如 ANCA 亞型、免疫球蛋白、感染關聯)對應。
選項分析
- 選項A (1)+(2)+(3)
- Granulomatosis with polyangiitis (GPA) 與 PR3-ANCA(cANCA)高度相關,>90% 患者呈現 cANCA(+)。正確 (en.wikipedia.org)
- Takayasu arteritis 常因主動脈弓大分支不對稱性狹窄,導致雙側肱動脈收縮壓差 >10 mmHg。正確 (pmc.ncbi.nlm.nih.gov)
- Giant cell arteritis (GCA) 發病年齡多在 >50 歲,年輕族群罕見;題中「年輕高盛行」錯誤。 ([en.wikipedia.org](https://en.wikipedia.org/wiki/Giant_cell_arteritis?utm_source=chat
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